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Wydanie 1/2016
str. 66 - 71

Okulistyczna manifestacja choroby Behçeta – opis przypadku

Ocular Manifestation of Behçet’s Disease – Case Report

Małgorzata Figurska¹, Izabela Jamiołkowska¹, Marek Rękas¹, Witold Tłustochowicz²

¹Klinika Okulistyki CSK MON
Wojskowy Instytut Medyczny w Warszawie
Kierownik: prof. dr hab. n. med. Marek Rękas ²Klinika Chorób Wewnętrznych i Reumatologii CSK MON
Wojskowy Instytut Medyczny w Warszawie
Kierownik: prof. dr hab. n. med. Witold Tłustochowicz

Summary: Behçet’s disease is a multi-system disorder of unknown etiology. Interdisciplinary cooperation in the assessment of patients is essential in order to perform a correct diagnosis. In this rare, in our latitude, disorder, small, medium and large vessels are affected and almost all systems can be affected. We present a case of Behçet’s disease with the critical ocular manifestation where the patient was diagnosed more than a year after the first mucocutaneous lesions manifested. Despite intensive immunosuppression involving complex biological agents, within six months bilateral chorioretinitis, vasculitis with optic nerve involvement and inflammatory reaction of vitreous were observed. As a result of inflammation, diffuse pigment epithelium and capillary atrophy occurred and permanent bilateral deterioration of hand-to-eye movement was observed. The patient remains under ophthalmological, rheumatological and neurological care. Immunosuppression through the use of biological agents is ongoing.

Słowa kluczowe: choroba Behceta, zapalenie naczyń siatkówki, immunosupresja, infliksimab, TNF-α.

Keywords: Behcet’s disease, retinal vasculitis, immunosuppression, infliximab TNF-α.

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